Castleman's Disease Associated with Pemphigus Vulgaris: Remains Retrospectively Diagnosed Entity
Castleman's disease is a rare, benign, lymphoproliferative disorder of unknown cause.[1] The disease can be occasionally associated with a paraneoplastic pemphigus (PNP), an autoimmune mucocutaneous disorder commonly seen in neoplasms of lymphocytic origin.[2] Castleman's tumor has been found in only 10 % of PNP patients,[3] so the diagnosis depends mainly on the pathological examination. For pathological examination, complete surgical excision biopsy of uni-centric disease remains best mode of treatment. We report a case of retrospectively diagnosed case of castleman’s disease with PNP after pathological examination.
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